Pure red cell aplasia in a patient with lupus-like disease and thymoma
نویسندگان
چکیده
Pure red cell aplasia (PRCA) is a rare complication of autoimmune rheumatic diseases such as systemic lupus erythematosus (SLE). Thymoma occurs in 5–13% of patients with PRCA and in 2% of patients with SLE. The simultaneous occurrence, however, of all 3 disorders is rare. We report a patient with lupus-like disease who developed PRCA in association with a thymoma and explore the management challenges that ensued.
منابع مشابه
Graft-versus-host disease-like erythroderma: a sign of recurrent thymoma
RATIONALE Thymomas are associated with numerous autoimmune disorders, such as myasthenia gravis (MG), pure red cell aplasia (PRCA), and systemic lupus erythematosus (SLE). However, graft-versus-host disease (GVHD)-like erythroderma is a relatively uncommon paraneoplastic disorder associated with thymomas and signifies a poor prognosis. PATIENT CONCERNS A 35-year-old woman with medical history...
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